A rare case of porokeratotic eccrine ostial and dermal duct nevus
Keywords:Porokeratosis, Nevus, Ecrine, Ostia
AbstractIntroduction: Porokeratotic eccrine ostial and dermal duct nevus (PEODDN) is an uncommon cutaneous condition, distinguished by numerous punctate pits and keratotic papules. Case report: A 25-year-old female presented with asymptomatic rough papules for the past 3 years. Clinical examination showed keratotic papules, distributed over right palm’s radial aspect, just below and in front of base of thumb. Similar lesions were found on the inner side of right foot. The histopathological features were typical of PEODDN. Discussion: PEODDN is characterized clinically by multiple linear punctuate pits with comedo like plugs on palms and soles. It can present at birth or early childhood or can occur late in life. It is typically asymptomatic with very few treatment options described in literature. Conclusion: It is an uncommon and cosmetically disfiguring condition with only a few case reports till date.
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