A clinicoepidemilogical study on icthyosis in a district hospital

Authors

  • Neerja Puri Punjab Health Systems Corporation, India.

Abstract

Objective To study the demography and clinical spectrum of icthyosis in children below twelve years of age.   Methods A prospective randomized hospital based study was conducted between June 2013 and June 2015 in a district hospital in North India. The children were thoroughly examined and routine investigations were carried out.   Results In two years duration, 2523 children coming to the dermatology OPD were screened for icthyosis.   Conclusion  There were 21 patients (70%) of icthyosis vulgaris, 3 patients(10%) of X linked recessive icthyosis, 2 patients (6.66%) of  lamellar icthyosis, 2 patients (6.66%) of  non bullous icthyosiform erythroderma, 1 patient (3.33%) of  bullous icthyosiform erythroderma and 1 patient (3.33%) of Netherton syndrome. Palmoplantar keratoderma was seen in 5 patients(16.66%), impairment of sweating was seen in 6 patients (20%), keratosis pilaris was seen in 3 patients (10%), atopic diathesis was seen in 3 patients (10%), colloidon membrane was seen in 2 patients (6.66%) and eye involvement  in the form of corneal opacity was seen in 1 patient (3.33%).  

References

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Published

2023-08-07

How to Cite

1.
Puri N. A clinicoepidemilogical study on icthyosis in a district hospital. J Pak Assoc Dermatol [Internet]. 2023Aug.7 [cited 2024May19];33(3):817-20. Available from: https://jpad.com.pk/index.php/jpad/article/view/2185

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