A case of xanthoma disseminatum: A rare type of non–Langerhans cell histiocytosis

Authors

  • ATM Asaduzzaman
  • Md. Mostaque Mahmud
  • Muhammad Raquib Rahman
  • MA Wahab
  • Nadia Sharleen

Keywords:

Non-Langerhans cell histiocytosis, xanthoma disseminatum

Abstract

Xanthoma disseminatum (XD) is a rare non-Langerhans cell histiocytosis that may involve skin, mucous membrane and internal organs. It manifests as symmetrically distributed, yellow-brown papules and nodules, involving face and flexures of body. We describe a case of XD in a 22-year-old female. She presented with multiple yellow-brown papules and plaques over face and body folds. Skin lesions were accompanied by visual disturbances. Examination revealed xanthomatous infiltration of cornea and oral mucosa. The case was confirmed with histopathological assessment. 

References

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Published

2018-12-13

How to Cite

1.
Asaduzzaman A, Mahmud MM, Rahman MR, Wahab M, Sharleen N. A case of xanthoma disseminatum: A rare type of non–Langerhans cell histiocytosis. J Pak Assoc Dermatol [Internet]. 2018Dec.13 [cited 2025Mar.23];28(3):371-4. Available from: https://jpad.com.pk/index.php/jpad/article/view/1271

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Case Reports

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