Naevus of Ota with Port Wine Stain – A rare entity

Sundeep Chowdhry, Neha Yadav, Dipak Umrigar, Akhilesh Shukla


Nevus of Ota, which was originally described by Ota and Tanino in 1939, is a hamartoma of dermal melanocytes. It, also known as nevus fuscoceruleus ophthalmomaxillaris, is a pigmentary change involving the first and second divisions of the trigeminal nerve. Patients with the nevus of Ota have increased amounts of melanin (pigment) and melanin producing cells (melanocytes). The melanocytosis also affects the oral cavity, nasal mucosa, external auditory canal, tympanic membrane, orbital fissures, meninges and the brain. A port-wine stain (PWS) is defined as a macular telangiectatic patch (CM) which is present at birth and persists throughout life. They may be localized or extensive, affecting a whole limb. Here, we report a rare case of co-existence of nevus of Ota and port-wine stain.



Nevus of ota, Portwine stain, Anterior staphyloma, Glaucoma

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