A sporadic case of ichthyosis hystrix: A rare entity

Meenakshi Garg, Masuma P Bhengra, Pawan Gupta, Shyam Sundar Chaudhary

Abstract


The term ichthyosis hystrix encompasses several rare ichthyosiform disorders characterized by massive hyperkeratosis with an appearance like spiny scales. This is a rare form of ichthyosis with autosomal dominant inheritance and a very few cases have been reported. We report a case of ichthyosis hystrix in a 22-year-old male patient with hyperkeratotic, dry, warty, scaly excrescences on most of the body surface in a linear pattern. Palms, soles and nails were spared and family history was negative. The case is being reported in view of the rarity of disease and its sporadic occurrence.

Keywords


Ichthyosis hystrix, hyperkeratosis, sporadic

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References


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ISSN: 1560-9014