A sporadic case of ichthyosis hystrix: A rare entity


  • Meenakshi Garg
  • Masuma P Bhengra
  • Pawan Gupta
  • Shyam Sundar Chaudhary


Ichthyosis hystrix, hyperkeratosis, sporadic


The term ichthyosis hystrix encompasses several rare ichthyosiform disorders characterized by massive hyperkeratosis with an appearance like spiny scales. This is a rare form of ichthyosis with autosomal dominant inheritance and a very few cases have been reported. We report a case of ichthyosis hystrix in a 22-year-old male patient with hyperkeratotic, dry, warty, scaly excrescences on most of the body surface in a linear pattern. Palms, soles and nails were spared and family history was negative. The case is being reported in view of the rarity of disease and its sporadic occurrence.


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