Urticaria pigmentosa in a child with sporadic bilateral diffuse conjunctival redness: Case report and review of the literature

Ali H. Al-Ghamdi, Ahmed Hassan Al-Ghamdi, Hasan S. Al-Ghamdi, Aziz A. Al-Sohaimi, Mesfer Al-Ghamdi

Abstract


We present a case of a 2-year-old girl with urticaria pigmentosa. The clinical features indicated disseminated, discrete, non-clustered, reddish-brown macules, papules, and plaques on her body (0.5-1 cm in diameter).  Skin lesions occurred in the second month of life. There was associated sporadic bilateral lid swelling, diffuse conjunctival redness, and watery discharge. Darier's sign was positive. Diagnosis of mastocytosis was confirmed histopathologically. To the best of our knowledge, this information has not been previously reported.

 


Keywords


Mast cells, mastocytosis, urticaria pigmentosa

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References


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